Bcs1l - BCS1 homolog, ubiquinol-cytochrome c reductase complex chaperone

Predicted to enable ATP binding activity. Predicted to be involved in mitochondrion organization. Predicted to be located in mitochondrion. Predicted to be active in mitochondrial inner membrane. Human ortholog(s) of this gene implicated in Bjornstad syndrome; GRACILE syndrome; and mitochondrial complex III deficiency nuclear type 1. Orthologous to human BCS1L (BCS1 homolog, ubiquinol-cytochrome c reductase complex chaperone). [provided by Alliance of Genome Resources, Apr 2022]