Lymphoplasmacytic Lymphoma (WM)

Alias:
Waldenstrom Macroglobulinemia
Waldenström Macroglobulinemia
Waldenstroem's Macroglobulinemia
Waldenström Macroglobulinaemia Without Mention of Remission
Lymphoplasmacytic Lymphoma with Igm Gammopathy
Malignant Lymphoma - Lymphoplasmacytic
Macroglobulinemia of Waldenstrom
Waldenstrom's Macroglobulinemia
Waldenström's Macroglobulinemia
Waldenström Macroglobulinaemia
Idiopathic Macroglobulinaemia
Primary Macroglobulinaemia
Wm Syndrome
Wm
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基础信息
疾病表征
基因 & 突变
靶点药物
疾病模型
文献报道
淋巴浆细胞淋巴瘤,又名瓦尔登斯特伦巨球蛋白血症,与巨球蛋白血症和伯基特淋巴瘤有关。与淋巴浆细胞淋巴瘤相关的重要基因是MYD88(MYD88先天性免疫信号转导适配子),其相关通路/超级通路包括ERK信号通路和Akt信号通路。在该疾病的背景下,提到了D-酪氨酸和氟达拉滨。附属组织包括骨髓和B细胞,相关表型为白血病和淋巴瘤。
Related ID:
MESH:D008258
ICD11:2058944823

Basic Information

Inheritance
Age of Onset
Prevalence
Related Gene
Related Mouse Models
Reference
MALACARDS
--
未知
1-9/1000000
27
360
3

Medical Symptom

#
Categorization
Description
HPO Frequency
Orphanet Frequency
HPO Source Accession
No data available

Gene & Mutation

#
Gene
Function
Score
Mutations
No data available

Related Drugs

Name
CAS Number
Status
Phase
No data available

Disease Model

Category
Name
MGI
Related Gene
Strain of Origin
Publications
No data available

References Literature

Title
PMID
Journal
Year
IF
No Data Found!
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