Kaposi Sarcoma

卡波西肉瘤易感性(来自ICD-11)
别称:
Kaposi's Sarcoma
Kaposi Sarcoma, Susceptibility to
Kaposi's Sarcoma of Soft Tissue
Kaposi's Sarcoma of Palate
Kaposi's Sarcoma of Lung
Multiple Idiopathic Pigmented Hemangiosarcoma, Susceptibility to
Multiple Idiopathic Pigmented Hemangiosarcoma
Kaposi's Sarcoma of Central Nervous System
Kaposi's Sarcoma of Gastrointestinal Sites
African Lymphadenopathic Kaposi's Sarcoma
Central Nervous System Kaposi's Sarcoma
Kaposi's Sarcoma-Associated Herpesvirus
Angiofollicular Ganglionic Hyperplasia
Kaposi's Sarcoma of the Gallbladder
Sarcoma, Kaposi, Susceptibility to
Lymphadenopathic Kaposi's Sarcoma
Multi-Centric Castleman's Disease
Kaposi's Sarcoma of Soft Tissues
Kaposi's Sarcoma of the Prostate
Kaposi's Sarcoma of Conjunctiva
Kaposi's Sarcoma of Lymph Nodes
Non-Aids-Related Kaposi Sarcoma
Conjunctival Kaposi's Sarcoma
Kaposi's Sarcoma of Esophagus
Gallbladder Kaposi's Sarcoma
Soft Tissue Kaposi's Sarcoma
Esophageal Kaposi's Sarcoma
Intestinal Kaposi's Sarcoma
Kaposi's Sarcoma of the Cns
Lymph Node Kaposi's Sarcoma
Cutaneous Kaposi's Sarcoma
Kaposi's Sarcoma of Cornea
Pulmonary Kaposi's Sarcoma
Kaposi's Sarcoma of Heart
Kaposi's Sarcoma of Penis
Prostate Kaposi's Sarcoma
Angiolymphoid Hyperplasia
Cardiac Kaposi's Sarcoma
Corneal Kaposi's Sarcoma
Gastric Kaposi's Sarcoma
Kaposi's Sarcoma of Anus
Kaposi's Sarcoma of Skin
Palate Kaposi's Sarcoma
Kaposi's Sarcoma, Lung
Kaposi's Sarcoma, Skin
Penis Kaposi's Sarcoma
Anal Kaposi's Sarcoma
Sarcoma, Kaposi
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基础信息
疾病表征
基因 & 突变
靶点药物
疾病模型
文献报道
卡波西肉瘤,又称卡波西氏肉瘤,与肉瘤和获得性免疫缺陷综合征有关,症状包括皮疹、瘙痒和发热。与卡波西肉瘤有关的重要基因是IL6(白介素6),其相关通路/超级通路包括先天免疫系统和ERK信号通路。在该疾病的背景下提到了苯佐卡因和博莱霉素。附属组织包括皮肤和肺,相关表型为复发性单纯疱疹和皮肤肿瘤
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相关ID:
MESH:D012514
ICD11:1617583339

基础信息

遗传方式
发病时间
患病率/发病率
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参考文献
MALACARDS
常显
成年期
1-9/100000
48
522
36

疾病表征

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靶点药物

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疾病模型

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MGI
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