Hemolytic Uremic Syndrome, Atypical 1 (AHUS1)

非典型性溶血尿毒症综合征易感性1型(来自ICD-11)

别称:

Atypical Hemolytic-Uremic Syndrome

Atypical Hemolytic Uremic Syndrome

Hemolytic Uremic Syndrome, Atypical, Susceptibility to, 1

Ahus

Hemolytic Uremic Syndrome, Atypical, Susceptibility to

Hemolytic-Uremic Syndrome

Atypical Hus

Ahus1

Hemolytic Uremic Syndrome Associated with Shiga Toxin-Producing Escherichia Coli

Atypical Hemolytic Uremic Syndrome with Anti-Factor H Antibodies

Atypical Hemolytic-Uremic Syndrome with Anti-Factor H Antibodies

Atypical Hemolytic Uremic Syndrome with H Factor Anomaly

Ahus with Neutralizing Autoantibodies Against Factor H

Shiga Toxin-Associated Hemolytic Uremic Syndrome

Hemolytic-Uremic Syndrome, Atypical, Type 1

Atypical Hus with Anti-Factor H Antibodies

Hemolytic-Uremic Syndrome Without Diarrhea

Hemolytic Uremic Syndrome with Diarrhea

Hemolytic Uremic Syndrome Atypical 1

Hemolytic Uremic Syndrome, Atypical

Non-Shiga-Like Toxin-Associated Hus

Ahus with Anti-Factor H Antibodies

Hemolytic Uremic Syndrome, Typical

Typical Hemolytic Uremic Syndrome

Shiga-Like Toxin-Associated Hus

Ahus, Susceptibility to, 1

Nonenteropathic Hus

Non-Stx-Hus

Typical Hus

Ehec-Hus

Stec-Hus

Stx-Hus

Ahus 1

D+ Hus

D Hus

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基础信息

疾病表征

基因 & 突变

靶点药物

疾病模型

文献报道

血栓性微血管病，非典型 1，又称非典型血栓性微血管病，与遗传性非典型血栓性微血管病和补体基因异常性非典型血栓性微血管病有关。血栓性微血管病，非典型 1 的一个重要基因是 CFH（补体因子 H），其相关通路/超通路包括先天性免疫系统和血液凝固疾病。在该疾病的背景下提到了 Eculizumab 和补体系统蛋白。附属组织包括肾脏和皮肤，相关表型为蛋白尿和血小板减少症。

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