Chronic Lymphoproliferative Disorder of Natural Killer Cells (CNKL)

Alias:
Nk-Cell Lineage Granular Lymphocyte Proliferative Disorder
Chronic Lymphoproliferative Disorder of Nk-Cells
Chronic Nk-Cell Lymphocytosis
Chronic Nk Lymphocytosis
Clpd-Nk
Cnkl
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基础信息
疾病表征
基因 & 突变
靶点药物
疾病模型
文献报道
自然杀伤细胞慢性增殖性疾病,又称为nk细胞系颗粒淋巴细胞增殖性疾病,与慢性nk细胞淋巴细胞增多症和淋巴增殖综合征有关。与自然杀伤细胞慢性增殖性疾病相关的重要基因是STAT3(信号转导和转录激活因子3)。在该疾病的背景下,已经提到了泼尼松和甲氨蝶呤。附属组织包括nk细胞和皮肤。
Related ID:
ICD11:921755282

Basic Information

Inheritance
Age of Onset
Prevalence
Related Gene
Related Mouse Models
Reference
MALACARDS
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未知
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1
23
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Medical Symptom

#
Categorization
Description
HPO Frequency
Orphanet Frequency
HPO Source Accession
No data available

Gene & Mutation

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Gene
Function
Score
Mutations
No data available

Related Drugs

Name
CAS Number
Status
Phase
No data available

Disease Model

Category
Name
MGI
Related Gene
Strain of Origin
Publications
No data available

References Literature

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PMID
Journal
Year
IF
No Data Found!
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