B-Lymphoblastic Leukemia/lymphoma with Tcf3-Pbx1

Alias:
B Acute Lymphoblastic Leukemia with T(1;19)(q23;p13.3); E2a-Pbx1 (tcf3-Pbx1)
B-Lymphoblastic Leukemia/lymphoma with T(1;19)(q23;p13.3);tcf3-Pbx1
B-All with Tcf3-Pbx1
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基础信息
疾病表征
基因 & 突变
靶点药物
疾病模型
文献报道
B淋巴母细胞白血病/淋巴瘤伴Tcf3-Pbx1,也称为b急性淋巴母细胞白血病伴t(1;19)(q23;p13.3); e2a-pbx1 (tcf3-pbx1),与b淋巴母细胞白血病/淋巴瘤伴t(1;19)(q23;p13.3)和未成熟急性髓系白血病有关。与B淋巴母细胞白血病/淋巴瘤伴Tcf3-Pbx1有关的重要基因是ZNF292(锌指蛋白292)。Fludarabine和Lenograstim已在这种疾病的背景下被提及。相关表型是shRNA丰度增加(Z分数> 2)。
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Basic Information

Inheritance
Age of Onset
Prevalence
Related Gene
Related Mouse Models
Reference
MALACARDS
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未知
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Medical Symptom

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Categorization
Description
HPO Frequency
Orphanet Frequency
HPO Source Accession
No data available

Gene & Mutation

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Gene
Function
Score
Mutations
No data available

Related Drugs

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CAS Number
Status
Phase
No data available

Disease Model

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Name
MGI
Related Gene
Strain of Origin
Publications
No data available

References Literature

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PMID
Journal
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