Angioimmunoblastic T-Cell Lymphoma (AILT)

Alias:
Immunoblastic Lymphadenopathy
T-Cell Lymphoma, Aild Type
Lymphogranulomatosis X
Ailt
Aild - [angioimmunoblastic Lymphadenopathy with Dysproteinaemia]
Angioimmunoblastic Lymphadenopathy
Angioimmunoblastic Lymphoma
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基础信息
疾病表征
基因 & 突变
靶点药物
疾病模型
文献报道
血管免疫母细胞性T细胞淋巴瘤,又名免疫性淋巴结病,与麻疹和淋巴瘤有关,症状包括麻疹。与血管免疫母细胞性T细胞淋巴瘤相关的重要基因是CXCL13(C-X-C趋化因子配体13),其相关通路/超级通路包括Akt信号通路和PAK通路。在该疾病的背景下提到了药物吡柔比星和吉西他滨。附属组织包括淋巴结和骨髓,相关表型为细胞和正常。
Related ID:
MESH:D007119
ICD11:1254954229

Basic Information

Inheritance
Age of Onset
Prevalence
Related Gene
Related Mouse Models
Reference
MALACARDS
--
成年期
<1/1000000
28
324
--

Medical Symptom

#
Categorization
Description
HPO Frequency
Orphanet Frequency
HPO Source Accession
No data available

Gene & Mutation

#
Gene
Function
Score
Mutations
No data available

Related Drugs

Name
CAS Number
Status
Phase
No data available

Disease Model

Category
Name
MGI
Related Gene
Strain of Origin
Publications
No data available

References Literature

Title
PMID
Journal
Year
IF
No Data Found!
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