Keratoendotheliitis Fugax Hereditaria, also known as keratitis fugax hereditaria, is related to cryopyrin-associated periodic syndrome and keratitis, hereditary. An important gene associated with Keratoendotheliitis Fugax Hereditaria is NLRP3 (NLR Family Pyrin Domain Containing 3). Affiliated tissues include eye and skin, and related phenotypes are keratitis and opacification of the corneal stroma