Enables amidinotransferase activity. Involved in several processes, including embryonic liver development; response to mercury ion; and response to peptide hormone. Predicted to be located in mitochondrial intermembrane space. Predicted to be active in mitochondrion. Biomarker of acute kidney failure. Human ortholog(s) of this gene implicated in AGAT deficiency and Fanconi renotubular syndrome 1. Orthologous to human GATM (glycine amidinotransferase). [provided by Alliance of Genome Resources, Apr 2022]