Mccc2 - methylcrotonoyl-Coenzyme A carboxylase 2 (beta)

Predicted to enable ATP binding activity and ligase activity. Predicted to contribute to methylcrotonoyl-CoA carboxylase activity. Predicted to be involved in coenzyme A metabolic process and leucine catabolic process. Located in mitochondrion. Is expressed in metanephros and spinal cord. Human ortholog(s) of this gene implicated in 3-Methylcrotonyl-CoA carboxylase 2 deficiency and mitochondrial metabolism disease. Orthologous to human MCCC2 (methylcrotonyl-CoA carboxylase subunit 2). [provided by Alliance of Genome Resources, Apr 2022]