Qrsl1 - glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1

Predicted to enable glutaminyl-tRNA synthase (glutamine-hydrolyzing) activity. Acts upstream of or within mitochondrial translation and regulation of protein stability. Located in mitochondrion. Human ortholog(s) of this gene implicated in combined oxidative phosphorylation deficiency 40. Orthologous to human QRSL1 (glutaminyl-tRNA amidotransferase subunit QRSL1). [provided by Alliance of Genome Resources, Apr 2022]