Trnt1 - tRNA nucleotidyl transferase, CCA-adding, 1

Predicted to enable ATP:3'-cytidine-cytidine-tRNA adenylyltransferase activity; tRNA binding activity; and tRNA nucleotidyltransferase activity. Predicted to be involved in mitochondrial tRNA 3'-end processing and tRNA 3'-terminal CCA addition. Predicted to act upstream of or within tRNA processing. Located in mitochondrion. Human ortholog(s) of this gene implicated in sideroblastic anemia with B-cell immunodeficiency, periodic fevers, and developmental delay. Orthologous to human TRNT1 (tRNA nucleotidyl transferase 1). [provided by Alliance of Genome Resources, Apr 2022]