Predicted to enable propionyl-CoA carboxylase activity. Located in mitochondrion. Is expressed in several structures, including adipose tissue; alimentary system; central nervous system; eye; and respiratory system. Human ortholog(s) of this gene implicated in amino acid metabolic disorder and propionic acidemia. Orthologous to human PCCB (propionyl-CoA carboxylase subunit beta). [provided by Alliance of Genome Resources, Apr 2022]