Predicted to be involved in mitochondrial respiratory chain complex I assembly. Located in mitochondrion. Is expressed in limb long bone; otic capsule; thoracic segment skeleton; and viscerocranium. Human ortholog(s) of this gene implicated in linear skin defects with multiple congenital anomalies 3 and nuclear type mitochondrial complex I deficiency 30. Orthologous to human NDUFB11 (NADH:ubiquinone oxidoreductase subunit B11). [provided by Alliance of Genome Resources, Apr 2022]