Ivd - isovaleryl coenzyme A dehydrogenase

Predicted to enable identical protein binding activity and isovaleryl-CoA dehydrogenase activity. Predicted to be involved in fatty acid beta-oxidation using acyl-CoA dehydrogenase and leucine catabolic process. Located in mitochondrion. Is expressed in several structures, including alimentary system; brain; ear; genitourinary system; and respiratory system. Human ortholog(s) of this gene implicated in amino acid metabolic disorder and isovaleric acidemia. Orthologous to human IVD (isovaleryl-CoA dehydrogenase). [provided by Alliance of Genome Resources, Apr 2022]