Auh - AU RNA binding methylglutaconyl-CoA hydratase

Predicted to enable enoyl-CoA hydratase activity and mRNA 3'-UTR binding activity. Predicted to be involved in fatty acid beta-oxidation. Predicted to be active in mitochondrion. Human ortholog(s) of this gene implicated in 3-methylglutaconic aciduria type 1 and renal tubular transport disease. Orthologous to human AUH (AU RNA binding methylglutaconyl-CoA hydratase). [provided by Alliance of Genome Resources, Apr 2022]