Nags - N-acetylglutamate synthase

Predicted to enable acetyl-CoA:L-glutamate N-acetyltransferase activity and arginine binding activity. Predicted to be involved in arginine biosynthetic process and glutamate metabolic process. Predicted to be located in mitochondrion. Predicted to be active in mitochondrial matrix. Human ortholog(s) of this gene implicated in N-acetylglutamate synthase deficiency and amino acid metabolic disorder. Orthologous to human NAGS (N-acetylglutamate synthase). [provided by Alliance of Genome Resources, Apr 2022]