Enables carnitine O-palmitoyltransferase activity. Involved in fatty acid beta-oxidation and response to fatty acid. Located in mitochondrion. Human ortholog(s) of this gene implicated in brain disease; lipid metabolism disorder; and muscular disease. Orthologous to human CPT2 (carnitine palmitoyltransferase 2). [provided by Alliance of Genome Resources, Apr 2022]