Enables ATP binding activity; biotin binding activity; and pyruvate carboxylase activity. Involved in carboxylic acid metabolic process; gluconeogenesis; and positive regulation of phospholipid biosynthetic process. Located in mitochondrion. Human ortholog(s) of this gene implicated in pyruvate carboxylase deficiency disease. Orthologous to human PC (pyruvate carboxylase). [provided by Alliance of Genome Resources, Apr 2022]