Coq7 - demethyl-Q 7

Predicted to enable 2-octoprenyl-3-methyl-6-methoxy-1,4-benzoquinone hydroxylase activity and chromatin binding activity. Acts upstream of or within several processes, including age-dependent response to oxidative stress; chordate embryonic development; and mitochondrion morphogenesis. Located in mitochondrion. Is expressed in several structures, including alimentary system; ear; nervous system; respiratory system; and skeleton. Human ortholog(s) of this gene implicated in primary coenzyme Q10 deficiency 8. Orthologous to human COQ7 (coenzyme Q7, hydroxylase). [provided by Alliance of Genome Resources, Apr 2022]