Ndufb11 - NADH:ubiquinone oxidoreductase subunit B11

Predicted to be involved in mitochondrial respiratory chain complex I assembly. Located in mitochondrion. Is expressed in several structures, including central nervous system; genitourinary system; hemolymphoid system gland; sensory organ; and trunk mesenchyme. Human ortholog(s) of this gene implicated in linear skin defects with multiple congenital anomalies 3 and nuclear type mitochondrial complex I deficiency 30. Orthologous to human NDUFB11 (NADH:ubiquinone oxidoreductase subunit B11). [provided by Alliance of Genome Resources, Apr 2022]