Ventricular Tachycardia, Catecholaminergic Polymorphic, 1, with or Without Atrial Dysfunction and/or Dilated Cardiomyopathy (CPVT1)

Ventricular Tachycardia, Catecholaminergic Polymorphic, 1, with or Without Atrial Dysfunction and/or Dilated Cardiomyopathy, also known as catecholaminergic polymorphic ventricular tachycardia 1, is related to idiopathic ventricular fibrillation, non brugada type and ventricular arrhythmias due to cardiac ryanodine receptor calcium release deficiency syndrome, and has symptoms including seizures and syncope. An important gene associated with Ventricular Tachycardia, Catecholaminergic Polymorphic, 1, with or Without Atrial Dysfunction and/or Dilated Cardiomyopathy is RYR2 (Ryanodine Receptor 2), and among its related pathways/superpathways are Transport of inorganic cations/anions and amino acids/oligopeptides and DREAM Repression and Dynorphin Expression. The drugs Calcium, Dietary and Calcium have been mentioned in the context of this disorder. Affiliated tissues include heart and atrioventricular node, and related phenotypes are bidirectional ventricular tachycardia and syncope