Vulvar Proximal-Type Epithelioid Sarcoma is related to epithelioid sarcoma and central nervous system angiosarcoma. An important gene associated with Vulvar Proximal-Type Epithelioid Sarcoma is SMARCB1 (SWI/SNF Related, Matrix Associated, Actin Dependent Regulator Of Chromatin, Subfamily B, Member 1), and among its related pathways/superpathways are Class I MHC mediated antigen processing and presentation and Keratinization. Related phenotype is Reduced mammosphere formation.