Septate Vagina, also known as congenital duplication of vagina, is related to müllerian duct anomalies-limb anomalies syndrome and uterus bicornis bicollis with partial vaginal septum and unilateral hematocolpos with ipsilateral renal agenesis. An important gene associated with Septate Vagina is WT1 (WT1 Transcription Factor). Affiliated tissues include uterus and cervix.