Rare Mitochondrial Non-Syndromic Sensorineural Deafness, also known as mitochondrial non-syndromic sensorineural hearing loss, is related to deafness, nonsyndromic sensorineural, mitochondrial and sensorineural hearing loss. An important gene associated with Rare Mitochondrial Non-Syndromic Sensorineural Deafness is MT-CO1 (Mitochondrially Encoded Cytochrome C Oxidase I).