Pyridoxine-Responsive Sideroblastic Anemia is related to anemia, sideroblastic, 1 and sideroblastic anemia. An important gene associated with Pyridoxine-Responsive Sideroblastic Anemia is ALAS2 (5'-Aminolevulinate Synthase 2), and among its related pathways/superpathways is Hemesynthesis defects and porphyrias. Affiliated tissues include bone marrow and bone.