Psoriasis 14, Pustular (PSORS14)

Psoriasis 14, Pustular(来自ICD-11)
别称:
Generalized Pustular Psoriasis
Gpp
Acrodermatitis Continua of Hallopeau
Ditra
Palmoplantar Pustulosis
Deficiency of the Interleukin-36 Receptor Antagonist
Interleukin 36 Receptor Antagonist Deficiency
Deficiency of Il-36r Antagonist
Pustular Psoriasis 14
Psors14
Psorp
Acrodermatitis Continua Suppurativa of Hallopeau
Generalized Pustular Psoriasis of Von Zumbusch
Pustular Psoriasis of the Palms and Soles
Acute Generalised Pustular Psoriasis
Acute Generalized Pustular Psoriasis
Pustulosis Palmaris Et Plantaris
Psoriasis, Pustular, Generalized
Palmoplantar Pustular Psoriasis
Ppp - [palmoplantar Pustulosis]
Pustulosis of Palms and Soles
Psoriasis, Pustular, Type 14
Von Zumbusch Psoriasis
Deficiency of Il-36ra
Pustular Bacterid
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Basic Information
Medical Symptom
Gene & Mutation
Related Drugs
Disease Model
References Literature
Psoriasis 14, Pustular, also known as generalized pustular psoriasis, is related to periodontitis, aggressive, 1 and sapho syndrome. An important gene associated with Psoriasis 14, Pustular is IL36RN (Interleukin 36 Receptor Antagonist), and among its related pathways/superpathways are Innate Immune System and MIF Mediated Glucocorticoid Regulation. The drugs Ixekizumab and Deucravacitinib have been mentioned in the context of this disorder. Affiliated tissues include skin and tongue, and related phenotypes are arthralgia and elevated erythrocyte sedimentation rate
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相关ID:
MESH:D011565
ICD11:877172115

基础信息

遗传方式
发病时间
患病率/发病率
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参考文献
MALACARDS
AR
Unknown
1-9/1000000
17
145
24

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靶点药物

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MGI
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