Primary Agammaglobulinemia

Primary Agammaglobulinemia, also known as antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia, is related to common variable immunodeficiency and agammaglobulinemia, x-linked. An important gene associated with Primary Agammaglobulinemia is TNFRSF13C (TNF Receptor Superfamily Member 13C), and among its related pathways/superpathways are TNF Superfamily - Human Ligand-Receptor Interactions and their Associated Functions and BAFF in B-Cell Signaling. The drugs Immunoglobulins and Immunoglobulins, Intravenous have been mentioned in the context of this disorder. Affiliated tissues include b cells.