Pancreatic Beta Cell Agenesis with Neonatal Diabetes Mellitus, also known as diabetes mellitus, insulin-dependent, neonatal, is related to neonatal diabetes and pancreatic agenesis 1. An important gene associated with Pancreatic Beta Cell Agenesis with Neonatal Diabetes Mellitus is KCNJ11 (Potassium Inwardly Rectifying Channel Subfamily J Member 11), and among its related pathways/superpathways are Integration of energy metabolism and AMP-activated protein kinase signaling. Affiliated tissues include pancreatic islet, and related phenotypes are neonatal insulin-dependent diabetes mellitus and abnormal abdomen morphology