Pancreatic Lipase Deficiency, also known as pancreatic triacylglycerol lipase deficiency, is related to hypercholesterolemia, familial, 1 and diarrhea. An important gene associated with Pancreatic Lipase Deficiency is PNLIP (Pancreatic Lipase). Affiliated tissues include lung, and related phenotypes are steatorrhea and exocrine pancreatic insufficiency