Pulmonary Arterial Hypertension Associated with Connective Tissue Disease

Pulmonary Arterial Hypertension Associated with Connective Tissue Disease, also known as pah associated with connective tissue disease, is related to pulmonary hypertension, primary, 1 and connective tissue disease. An important gene associated with Pulmonary Arterial Hypertension Associated with Connective Tissue Disease is HLA-B (Major Histocompatibility Complex, Class I, B). The drugs Bosentan and Endothelin Receptor Antagonists have been mentioned in the context of this disorder. Affiliated tissues include heart and lung.