Pulmonary Arterial Hypertension Associated with Portal Hypertension (POPH)

Pulmonary Arterial Hypertension Associated with Portal Hypertension, also known as portopulmonary hypertension, is related to hepatopulmonary syndrome and liver cirrhosis. The drugs Macitentan and Endothelin Receptor Antagonists have been mentioned in the context of this disorder. Affiliated tissues include liver and heart.