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ENPulmonary Systemic Sclerosis
Alias:
Lung Involvement in Systemic Sclerosis
Lung Disease with Systemic Sclerosis
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Pulmonary Systemic Sclerosis, also known as lung involvement in systemic sclerosis, is related to pulmonary hypertension, primary, 1 and scleroderma, familial progressive. An important gene associated with Pulmonary Systemic Sclerosis is TMSB4X (Thymosin Beta 4 X-Linked), and among its related pathways/superpathways is CCR3 Pathway in Eosinophils. The drugs Leuprolide and Cyclophosphamide have been mentioned in the context of this disorder. Affiliated tissues include lung and skin.
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MALACARDS
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