Phocomelia-Ectrodactyly-Deafness-Sinus Arrhythmia Syndrome, also known as phocomelia-ectrodactyly-hearing loss-sinus arrhythmia syndrome, is related to phocomelia-ectrodactyly, ear malformation, deafness, and sinus arrhythmia. Affiliated tissues include bone, and related phenotypes are microtia and abnormal nasal morphology