Neuronopathy, Distal Hereditary Motor, Autosomal Recessive 9, also known as neuropathy, distal hereditary motor, autosomal recessive 9, is related to coenzyme q10 deficiency, primary, 8. An important gene associated with Neuronopathy, Distal Hereditary Motor, Autosomal Recessive 9 is COQ7 (Coenzyme Q7, Hydroxylase).