Myelofibrosis (MYELOF)

Myelofibrosis(来自ICD-11)
别称:
Primary Myelofibrosis
Myelofibrosis with Myeloid Metaplasia
Agnogenic Myeloid Metaplasia
Idiopathic Myelofibrosis
Osteomyelofibrosis
Myeloid Metaplasia
Chronic Idiopathic Myelofibrosis
Megakaryocytic Myelosclerosis
Myelofibrosis, Idiopathic
Myelosclerosis
Agnogenic Myeloid Metaplasia with Myelofibrosis
Myelofibrosis, with Myeloid Metaplasia, Somatic
Myelofibrosis with Myeloid Metaplasia, Somatic
Myelosclerosis with Myeloid Metaplasia
Myelofibrosis, Somatic
Bone Marrow Fibrosis
Aleukemic Myelosis
Myelofibrosis Nos
Myelof
Ammm
Mmm
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Basic Information
Medical Symptom
Gene & Mutation
Related Drugs
Disease Model
References Literature
Myelofibrosis, also known as primary myelofibrosis, is related to myeloproliferative neoplasm and thrombocytosis. An important gene associated with Myelofibrosis is MPL (MPL Proto-Oncogene, Thrombopoietin Receptor), and among its related pathways/superpathways are TGF-Beta Pathway and PAK Pathway. The drugs Lactitol and Lenograstim have been mentioned in the context of this disorder. Affiliated tissues include bone marrow and myeloid, and related phenotypes are abnormal bone marrow cell morphology and splenomegaly
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相关ID:
MESH:D009191
ICD11:336704235

基础信息

遗传方式
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参考文献
MALACARDS
--
Adult
1-9/100000
89
1134
37

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MGI
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