Malignant Triton Tumor (MTT)

Alias:

Malignant Peripheral Nerve Sheath Tumor with Rhabdomyosarcomatous Differenciation

Malignant Peripheral Nerve Sheath Tumor with Rhabdomyoblastic Differentiation

Malignant Peripheral Nerve Sheath Neoplasm with Rhabdomyosarcoma

Mpnst with Rhabdomyosarcomatous Differentiation

Mpnst with Rhabdomyoblastic Differentiation

Mpnst with Rhabdomyosarcoma

Malignant Triton Tumour

Mtt

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Basic Information

Medical Symptom

Gene & Mutation

Related Drugs

Disease Model

References Literature

Malignant Triton Tumor, also known as malignant peripheral nerve sheath tumor with rhabdomyosarcomatous differenciation, is related to neurofibromatosis, type i and malignant peripheral nerve sheath tumor. An important gene associated with Malignant Triton Tumor is HTRA1 (HtrA Serine Peptidase 1), and among its related pathways/superpathways are Mesenchymal Stem Cells and Lineage-specific Markers and Pathophysiological roles of DUX4 in FSHD1. The drugs Ifosfamide and Doxorubicin have been mentioned in the context of this disorder. Affiliated tissues include small intestine and lung, and related phenotypes are Increased viability and muscle

Related ID：

MALACARDS：MLG041