Lymphoplasmacytic Lymphoma (WM)

Alias:
Waldenstrom Macroglobulinemia
Waldenström Macroglobulinemia
Waldenstroem's Macroglobulinemia
Waldenström Macroglobulinaemia Without Mention of Remission
Lymphoplasmacytic Lymphoma with Igm Gammopathy
Malignant Lymphoma - Lymphoplasmacytic
Macroglobulinemia of Waldenstrom
Waldenstrom's Macroglobulinemia
Waldenström's Macroglobulinemia
Waldenström Macroglobulinaemia
Idiopathic Macroglobulinaemia
Primary Macroglobulinaemia
Wm Syndrome
Wm
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Basic Information
Medical Symptom
Gene & Mutation
Related Drugs
Disease Model
References Literature
Lymphoplasmacytic Lymphoma, also known as waldenstrom macroglobulinemia, is related to macroglobulinemia and burkitt lymphoma. An important gene associated with Lymphoplasmacytic Lymphoma is MYD88 (MYD88 Innate Immune Signal Transduction Adaptor), and among its related pathways/superpathways are ERK Signaling and Akt Signaling. The drugs D-Tyrosine and Fludarabine have been mentioned in the context of this disorder. Affiliated tissues include bone marrow and b cells, and related phenotypes are leukemia and lymphoma
Related ID:
MESH:D008258
ICD11:2058944823

Basic Information

Inheritance
Age of Onset
Prevalence
Related Gene
Related Mouse Models
Reference
MALACARDS
--
Unknown
1-9/1000000
27
360
3

Medical Symptom

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Categorization
Description
HPO Frequency
Orphanet Frequency
HPO Source Accession
No data available

Gene & Mutation

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Mutations
No data available

Related Drugs

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Status
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No data available

Disease Model

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Name
MGI
Related Gene
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Publications
No data available

References Literature

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PMID
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IF
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