Lymphoplasmacytic Lymphoma (WM)

Lymphoplasmacytic Lymphoma(来自ICD-11)
别称:
Waldenstrom Macroglobulinemia
Waldenström Macroglobulinemia
Waldenstroem's Macroglobulinemia
Waldenström Macroglobulinaemia Without Mention of Remission
Lymphoplasmacytic Lymphoma with Igm Gammopathy
Malignant Lymphoma - Lymphoplasmacytic
Macroglobulinemia of Waldenstrom
Waldenstrom's Macroglobulinemia
Waldenström's Macroglobulinemia
Waldenström Macroglobulinaemia
Idiopathic Macroglobulinaemia
Primary Macroglobulinaemia
Wm Syndrome
Wm
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Basic Information
Medical Symptom
Gene & Mutation
Related Drugs
Disease Model
References Literature
Lymphoplasmacytic Lymphoma, also known as waldenstrom macroglobulinemia, is related to macroglobulinemia and burkitt lymphoma. An important gene associated with Lymphoplasmacytic Lymphoma is MYD88 (MYD88 Innate Immune Signal Transduction Adaptor), and among its related pathways/superpathways are ERK Signaling and Akt Signaling. The drugs D-Tyrosine and Fludarabine have been mentioned in the context of this disorder. Affiliated tissues include bone marrow and b cells, and related phenotypes are leukemia and lymphoma
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相关ID:
MESH:D008258
ICD11:2058944823

基础信息

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参考文献
MALACARDS
--
Unknown
1-9/100000
27
360
3

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