Langerhans Cell Histiocytosis (LCH)

Langerhans Cell Histiocytosis(来自ICD-11)
别称:
Histiocytosis X
Langerhans Cell Granulomatosis
Histiocytosis, Langerhans-Cell
Langerhans-Cell Histiocytosis
Hashimoto-Pritzger Disease
Letterer-Siwe Disease
Lch
Letterer-Siwe Disease Involving Lymph Nodes of Inguinal Region and Lower Limb
Letterer-Siwe Disease of Lymph Nodes of Inguinal Region Amd/or Lower Limb
Letterer-Siwe Disease of Lymph Nodes of Inguinal Region and/or Lower Limb
Letterer-Siwe Disease of Lymph Nodes of Inguinal Region and Lower Limb
Letterer-Siwe Disease Involving Lymph Nodes of Axilla and Upper Limb
Letterer-Siwe Disease Involving Lymph Nodes of Head, Face, and Neck
Letterer-Siwe Disease Involving Lymph Nodes of Head, Face and Neck
Letterer-Siwe Disease of Lymph Nodes of Axilla and/or Upper Limb
Letterer-Siwe Disease of Lymph Nodes of Head, Face and/or Neck
Letterer-Siwe Disease Involving Lymph Nodes of Multiple Sites
Letterer-Siwe Disease of Lymph Nodes of Axilla and Upper Limb
Letterer-Siwe Disease Involving Intra-Abdominal Lymph Nodes
Letterer-Siwe Disease of Lymph Nodes of Head, Face and Neck
Letterer-Siwe Disease Involving Intrathoracic Lymph Nodes
Letterer-Siwe Disease Involving Intrapelvic Lymph Nodes
Letterer-Siwe Disease of Lymph Nodes of Multiple Sites
Letterer-Siwe Disease of Intra-Abdominal Lymph Nodes
Letterer-Siwe Disease of Intrathoracic Lymph Nodes
Letterer-Siwe Disease of Intrapelvic Lymph Nodes
Letterer-Siwe Disease Involving Spleen
Langerhans-Cell Histiocytosis Nos
Letterer-Siwe Disease of Spleen
Langerhan's Cell Histiocytosis
Familial Letterer-Siwe Disease
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Basic Information
Medical Symptom
Gene & Mutation
Related Drugs
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References Literature
Langerhans Cell Histiocytosis, also known as histiocytosis x, is related to non-langerhans-cell histiocytosis and histiocytosis, and has symptoms including fever An important gene associated with Langerhans Cell Histiocytosis is BRAF (B-Raf Proto-Oncogene, Serine/Threonine Kinase), and among its related pathways/superpathways are MIF Mediated Glucocorticoid Regulation and Class I MHC mediated antigen processing and presentation. The drugs Mycophenolic acid and Anti-Infective Agents have been mentioned in the context of this disorder. Affiliated tissues include spleen and bone marrow, and related phenotypes are immune system and respiratory system
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相关ID:
MESH:C538636
ICD11:216625985

基础信息

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参考文献
MALACARDS
--
All ages
1-9/100000
38
510
5

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