Langerhans Cell Histiocytosis (LCH)

Alias:

Histiocytosis X

Langerhans Cell Granulomatosis

Histiocytosis, Langerhans-Cell

Langerhans-Cell Histiocytosis

Hashimoto-Pritzger Disease

Letterer-Siwe Disease

Lch

Letterer-Siwe Disease Involving Lymph Nodes of Inguinal Region and Lower Limb

Letterer-Siwe Disease of Lymph Nodes of Inguinal Region Amd/or Lower Limb

Letterer-Siwe Disease of Lymph Nodes of Inguinal Region and/or Lower Limb

Letterer-Siwe Disease of Lymph Nodes of Inguinal Region and Lower Limb

Letterer-Siwe Disease Involving Lymph Nodes of Axilla and Upper Limb

Letterer-Siwe Disease Involving Lymph Nodes of Head, Face, and Neck

Letterer-Siwe Disease Involving Lymph Nodes of Head, Face and Neck

Letterer-Siwe Disease of Lymph Nodes of Axilla and/or Upper Limb

Letterer-Siwe Disease of Lymph Nodes of Head, Face and/or Neck

Letterer-Siwe Disease Involving Lymph Nodes of Multiple Sites

Letterer-Siwe Disease of Lymph Nodes of Axilla and Upper Limb

Letterer-Siwe Disease Involving Intra-Abdominal Lymph Nodes

Letterer-Siwe Disease of Lymph Nodes of Head, Face and Neck

Letterer-Siwe Disease Involving Intrathoracic Lymph Nodes

Letterer-Siwe Disease Involving Intrapelvic Lymph Nodes

Letterer-Siwe Disease of Lymph Nodes of Multiple Sites

Letterer-Siwe Disease of Intra-Abdominal Lymph Nodes

Letterer-Siwe Disease of Intrathoracic Lymph Nodes

Letterer-Siwe Disease of Intrapelvic Lymph Nodes

Letterer-Siwe Disease Involving Spleen

Langerhans-Cell Histiocytosis Nos

Letterer-Siwe Disease of Spleen

Langerhan's Cell Histiocytosis

Familial Letterer-Siwe Disease

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Basic Information

Medical Symptom

Gene & Mutation

Related Drugs

Disease Model

References Literature

Langerhans Cell Histiocytosis, also known as histiocytosis x, is related to non-langerhans-cell histiocytosis and histiocytosis, and has symptoms including fever An important gene associated with Langerhans Cell Histiocytosis is BRAF (B-Raf Proto-Oncogene, Serine/Threonine Kinase), and among its related pathways/superpathways are MIF Mediated Glucocorticoid Regulation and Class I MHC mediated antigen processing and presentation. The drugs Mycophenolic acid and Anti-Infective Agents have been mentioned in the context of this disorder. Affiliated tissues include spleen and bone marrow, and related phenotypes are immune system and respiratory system

Related ID：

MALACARDS：LNG108

OMIM：604856

MESH：C538636

ICD11：216625985