Islet Cell Tumor

Alias:
Well Differentiated Pancreatic Endocrine Tumor
Malignant Neoplasm of Endocrine Pancreas
Malignant Tumour of Endocrine Pancreas
Malignant Pancreatic Endocrine Tumour
Malignant Tumor of Endocrine Pancreas
Malignant Pancreatic Endocrine Tumor
Pancreatic Endocrine Carcinoma
Pancreatic Endocrine Neoplasm
Endocrine Pancreas Cancer
Islet Cell Neoplasm
Adenoma, Islet Cell
Islet Cell Tumour
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Basic Information
Medical Symptom
Gene & Mutation
Related Drugs
Disease Model
References Literature
Islet Cell Tumor, also known as well differentiated pancreatic endocrine tumor, is related to mahvash disease and vipoma. An important gene associated with Islet Cell Tumor is SST (Somatostatin), and among its related pathways/superpathways are GPCR downstream signalling and Class A/1 (Rhodopsin-like receptors). The drugs Lutetium Lu 177 dotatate and Copper have been mentioned in the context of this disorder. Affiliated tissues include pancreas and pancreatic islet, and related phenotypes are homeostasis/metabolism and nervous system
Related ID:
MESH:D007516

Basic Information

Inheritance
Age of Onset
Prevalence
Related Gene
Related Mouse Models
Reference
MALACARDS
AD
Adult
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22
287
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Medical Symptom

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Categorization
Description
HPO Frequency
Orphanet Frequency
HPO Source Accession
No data available

Gene & Mutation

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Mutations
No data available

Related Drugs

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CAS Number
Status
Phase
No data available

Disease Model

Category
Name
MGI
Related Gene
Strain of Origin
Publications
No data available

References Literature

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PMID
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IF
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