Islet Cell Tumor

Islet Cell Tumor(来自ICD-11)
别称:
Well Differentiated Pancreatic Endocrine Tumor
Malignant Neoplasm of Endocrine Pancreas
Malignant Tumour of Endocrine Pancreas
Malignant Pancreatic Endocrine Tumour
Malignant Tumor of Endocrine Pancreas
Malignant Pancreatic Endocrine Tumor
Pancreatic Endocrine Carcinoma
Pancreatic Endocrine Neoplasm
Endocrine Pancreas Cancer
Islet Cell Neoplasm
Adenoma, Islet Cell
Islet Cell Tumour
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Basic Information
Medical Symptom
Gene & Mutation
Related Drugs
Disease Model
References Literature
Islet Cell Tumor, also known as well differentiated pancreatic endocrine tumor, is related to mahvash disease and vipoma. An important gene associated with Islet Cell Tumor is SST (Somatostatin), and among its related pathways/superpathways are GPCR downstream signalling and Class A/1 (Rhodopsin-like receptors). The drugs Lutetium Lu 177 dotatate and Copper have been mentioned in the context of this disorder. Affiliated tissues include pancreas and pancreatic islet, and related phenotypes are homeostasis/metabolism and nervous system
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相关ID:
MESH:D007516

基础信息

遗传方式
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参考文献
MALACARDS
AD
Adult
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22
287
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靶点药物

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临床阶段
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MGI
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