Insulinomatosis and Diabetes Mellitus, also known as islet cell adenomatosis, is related to insulinoma and hyperinsulinemic hypoglycemia, familial, 2. An important gene associated with Insulinomatosis and Diabetes Mellitus is MAFA (MAF BZIP Transcription Factor A). The drugs Octreotide and Somatostatin have been mentioned in the context of this disorder. Affiliated tissues include pancreatic islet, and related phenotypes are type ii diabetes mellitus and insulinoma