Ichthyosis, Congenital, Autosomal Recessive 10, also known as autosomal recessive congenital ichthyosis 10, is related to ichthyosis, congenital, autosomal recessive 1. An important gene associated with Ichthyosis, Congenital, Autosomal Recessive 10 is PNPLA1 (Patatin Like Phospholipase Domain Containing 1). Affiliated tissues include skin, and related phenotypes are palmoplantar keratoderma and erythroderma