Fatal Congenital Hypertrophic Cardiomyopathy Due to Glycogen Storage Disease, also known as fatal congenital hypertrophic cardiomyopathy due to glycogenosis, is related to glycogen storage disease of heart, lethal congenital. An important gene associated with Fatal Congenital Hypertrophic Cardiomyopathy Due to Glycogen Storage Disease is PRKAG2 (Protein Kinase AMP-Activated Non-Catalytic Subunit Gamma 2). Affiliated tissues include skeletal muscle.