Familial Isolated Arrhythmogenic Right Ventricular Dysplasia, also known as familial isolated arrhythmogenic right ventricular cardiomyopathy, is related to familial isolated arrhythmogenic ventricular dysplasia, right dominant form and familial isolated arrhythmogenic ventricular dysplasia, left dominant form. An important gene associated with Familial Isolated Arrhythmogenic Right Ventricular Dysplasia is DSP (Desmoplakin), and among its related pathways/superpathways are DREAM Repression and Dynorphin Expression and Keratinization. Affiliated tissues include heart, and related phenotypes are muscle and cardiovascular system