Follicular Dendritic Cell Sarcoma

Alias:
Dendritic Cell Sarcoma, Follicular
Dendritic Cell Sarcoma
Dendritic Cell Sarcoma, Not Otherwise Specified
Dendritic Cell Sarcoma, Interdigitating
Follicular Dendritic Cell Tumour
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Basic Information
Medical Symptom
Gene & Mutation
Related Drugs
Disease Model
References Literature
Follicular Dendritic Cell Sarcoma, also known as dendritic cell sarcoma, follicular, is related to castleman disease and igg4-related disease, and has symptoms including fatigue, fever and night sweats. An important gene associated with Follicular Dendritic Cell Sarcoma is CR1 (Complement C3b/C4b Receptor 1 (Knops Blood Group)), and among its related pathways/superpathways are Innate Immune System and Class I MHC mediated antigen processing and presentation. The drugs Pembrolizumab and Immune Checkpoint Inhibitors have been mentioned in the context of this disorder. Affiliated tissues include spleen and lung, and related phenotype is immune system.
Related ID:
MESH:D054740
ICD11:15445528

Basic Information

Inheritance
Age of Onset
Prevalence
Related Gene
Related Mouse Models
Reference
MALACARDS
--
All ages
<1/1000000
15
83
--

Medical Symptom

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Categorization
Description
HPO Frequency
Orphanet Frequency
HPO Source Accession
No data available

Gene & Mutation

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Gene
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No data available

Related Drugs

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CAS Number
Status
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No data available

Disease Model

Category
Name
MGI
Related Gene
Strain of Origin
Publications
No data available

References Literature

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PMID
Journal
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IF
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