Epidermolysis Bullosa, Lethal Acantholytic, also known as lethal acantholytic epidermolysis bullosa, is related to arrhythmogenic right ventricular dysplasia, familial, 8 and cardiomyopathy, dilated, with woolly hair and keratoderma, and has symptoms including onychomadesis An important gene associated with Epidermolysis Bullosa, Lethal Acantholytic is DSP (Desmoplakin). Affiliated tissues include skin and heart, and related phenotypes are sandal gap and abnormal blistering of the skin