Deafness, Autosomal Recessive 118, with Cochlear Aplasia, is also known as dfnb118. An important gene associated with Deafness, Autosomal Recessive 118, with Cochlear Aplasia is DFNB118 (Deafness, Autosomal Recessive 118, With Cochlear Aplasia). Affiliated tissues include brain, and related phenotypes are congenital sensorineural hearing impairment and cochlear aplasia