Deafness, Autosomal Recessive 40, also known as autosomal recessive nonsyndromic deafness 40, is related to deafness, autosomal recessive and spinocerebellar ataxia, autosomal recessive 8. An important gene associated with Deafness, Autosomal Recessive 40 is DFNB40 (Deafness, Autosomal Recessive 40). Related phenotypes are nervous system and hearing/vestibular/ear