Deafness, Autosomal Recessive 55, also known as autosomal recessive nonsyndromic deafness 55, is related to deafness, autosomal recessive and spinocerebellar ataxia, autosomal recessive 8. An important gene associated with Deafness, Autosomal Recessive 55 is DFNB55 (Deafness, Autosomal Recessive 55). Related phenotypes are hearing impairment and abnormal retinal morphology