Cardiomyopathy, Dilated, with Woolly Hair, Keratoderma, and Tooth Agenesis, also known as dcwhkta, is related to cardiomyopathy, dilated, with woolly hair and keratoderma and keratosis palmoplantaris striata ii. An important gene associated with Cardiomyopathy, Dilated, with Woolly Hair, Keratoderma, and Tooth Agenesis is DSP (Desmoplakin). Related phenotypes are ichthyosis and pruritus